TY - JOUR AU - Bach, Kathrin AU - Dohnálek, Jan AU - Škerlová, Jana AU - Kuzmík, Ján AU - Poláchová, Edita AU - Stanchev, Stancho AU - Majer, Pavel AU - Fanfrlík, Jindřich AU - Pecina, Adam AU - Řezáč, Jan AU - Lepšík, Martin AU - Borshchevskiy, Valentin AU - Polovinkin, Vitaly AU - Strisovsky, Kvido TI - Extensive targeting of chemical space at the prime side of ketoamide inhibitors of rhomboid proteases by branched substituents empowers their selectivity and potency JO - European journal of medicinal chemistry VL - 275 SN - 0009-4374 CY - Amsterdam [u.a.] PB - Elsevier Science M1 - FZJ-2025-00499 SP - 116606 - PY - 2024 AB - Rhomboid intramembrane serine proteases have been implicated in several pathologies, and emerge as attractive pharmacological target candidates. The most potent and selective rhomboid inhibitors available to date are peptidyl α-ketoamides, but their selectivity for diverse rhomboid proteases and strategies to modulate it in relevant contexts are poorly understood. This gap, together with the lack of suitable in vitro models, hinders ketoamide development for relevant eukaryotic rhomboid enzymes. Here we explore the structure-activity relationship principles of rhomboid inhibiting ketoamides by medicinal chemistry and enzymatic in vitro and in-cell assays with recombinant rhomboid proteases GlpG, human mitochondrial rhomboid PARL and human RHBDL2. We use X-ray crystallography in lipidic cubic phase to understand the binding mode of one of the best ketoamide inhibitors synthesized here containing a branched terminal substituent bound to GlpG. In addition, to extend the interpretation of the co-crystal structure, we use quantum mechanical calculations and quantify the relative importance of interactions along the inhibitor molecule. These combined experimental analyses implicates that more extensive exploration of chemical space at the prime side is unexpectedly powerful for the selectivity of rhomboid inhibiting ketoamides. Together with variations in the peptide sequence at the non-prime side, or its non-peptidic alternatives, this strategy enables targeted tailoring of potent and selective ketoamides towards diverse rhomboid proteases including disease-relevant ones such as PARL and RHBDL2. LB - PUB:(DE-HGF)16 C6 - 38901105 UR - <Go to ISI:>//WOS:001347413400001 DO - DOI:10.1016/j.ejmech.2024.116606 UR - https://juser.fz-juelich.de/record/1037154 ER -