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@ARTICLE{Leliveld:59552,
author = {Leliveld, S. R. and Korth, C.},
title = {{T}he use of conformation-specific ligands and assays to
dissect the molecular mechanisms of neurodegenerative
diseases},
journal = {Journal of neuroscience research},
volume = {85},
issn = {0360-4012},
address = {New York, NY [u.a.]},
publisher = {Wiley-Liss},
reportid = {PreJuSER-59552},
pages = {2285 - 2297},
year = {2007},
note = {Record converted from VDB: 12.11.2012},
abstract = {The use of conformation-specific ligands has been closely
linked to progress in the molecular characterization of
neurodegenerative diseases. Deposition of misfolded or
misprocessed proteins is now recognized as a hallmark of all
neurodegenerative diseases. Initially, dyes like Congo red
and thioflavin T were used as crudely conformation-specific
ligands for staining the beta-sheeted protein components of
amyloid deposits in neurodegenerative diseases such as
Alzheimer disease (AD) and prion disease, the two diseases
in which protein conformations were distinguished early on.
This conformational characterization of extracellular
protein deposits with dyes ultimately led to the
identification of key players in the disease processes. The
recent discovery of intermediate conformational species,
i.e., soluble oligomers for AD and PK-sensitive PrP(Sc) for
prion disease, whose conformation and assembly are thought
to be distinct from both the physiological and the fibrillar
conformational states, replaced the former notion that the
microscopic protein deposits themselves caused disease. This
insight and the generation of conformation-specific
monoclonal antibodies to these conformers further advanced
diagnosis and the understanding of molecular mechanisms of
AD and are likely to do so in other neurodegenerative
diseases. Here we review how conformer distinction performed
by a variety of different techniques, including biophysical,
biochemical, and antibody-based methods, led to the current
molecular concepts of AD and the prion diseases. We provide
an outlook on the application of these techniques in
advancing the understanding of molecular mechanisms of other
neurodegenerative diseases or degenerative brain
conditions.},
keywords = {Amyloid beta-Peptides: chemistry / Animals / Antibodies,
Monoclonal / Brain: pathology / Brain Chemistry / Humans /
Ligands / Neurodegenerative Diseases: diagnosis /
Neurodegenerative Diseases: pathology / Peptides: chemistry
/ PrPSc Proteins: chemistry / Protein Conformation / Amyloid
beta-Peptides (NLM Chemicals) / Antibodies, Monoclonal (NLM
Chemicals) / Ligands (NLM Chemicals) / Peptides (NLM
Chemicals) / PrPSc Proteins (NLM Chemicals) / J (WoSType)},
cin = {INB-2},
ddc = {570},
cid = {I:(DE-Juel1)VDB805},
pnm = {Funktion und Dysfunktion des Nervensystems},
pid = {G:(DE-Juel1)FUEK409},
shelfmark = {Neurosciences},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:17497676},
UT = {WOS:000248971500001},
doi = {10.1002/jnr.21353},
url = {https://juser.fz-juelich.de/record/59552},
}