% IMPORTANT: The following is UTF-8 encoded. This means that in the presence
% of non-ASCII characters, it will not work with BibTeX 0.99 or older.
% Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or
% “biber”.
@ARTICLE{Szeg:909067,
author = {Szegő, Éva M and Boß, Fabian and Komnig, Daniel and
Gärtner, Charlott and Höfs, Lennart and Shaykhalishahi,
Hamed and Wördehoff, Michael M and Saridaki, Theodora and
Schulz, Jörg B and Hoyer, Wolfgang and Falkenburger, Björn
H},
title = {{A} β-{W}rapin {T}argeting the {N}-{T}erminus of
α-{S}ynuclein {M}onomers {R}educes {F}ibril-{I}nduced
{A}ggregation in {N}eurons.},
journal = {Frontiers in neuroscience},
volume = {15},
issn = {1662-453X},
address = {Lausanne},
publisher = {Frontiers Research Foundation},
reportid = {FZJ-2022-02985},
pages = {696440},
year = {2021},
abstract = {Reducing α-synuclein pathology constitutes a plausible
strategy against Parkinson's disease. As we recently
demonstrated, the β-wrapin protein AS69 binds an N-terminal
region in monomeric α-synuclein, interferes with fibril
nucleation, and reduces α-synuclein aggregation in vitro
and in a fruit fly model of α-synuclein toxicity. The aim
of this study was to investigate whether AS69 also reduces
α-synuclein pathology in mammalian neurons. To induce
α-synuclein pathology, primary mouse neurons were exposed
to pre-formed fibrils (PFF) of human α-synuclein. PFF were
also injected into the striatum of A30P-α-synuclein
transgenic mice. The extent of α-synuclein pathology was
determined by phospho-α-synuclein staining and by Triton
X-100 solubility. The degeneration of neuronal somata,
dendrites, and axon terminals was determined by
immunohistochemistry. AS69 and PFF were taken up by primary
neurons. AS69 did not alter PFF uptake, but AS69 did reduce
PFF-induced α-synuclein pathology. PFF injection into mouse
striatum led to α-synuclein pathology and dystrophic
neurites. Co-injection of AS69 abrogated PFF-induced
pathology. AS69 also reduced the PFF-induced degeneration of
dopaminergic axon terminals in the striatum and the
degeneration of dopaminergic dendrites in the substantia
nigra pars reticulata. AS69 reduced the activation of
astroglia but not microglia in response to PFF injection.
Collectively, AS69 reduced PFF-induced α-synuclein
pathology and the associated neurodegeneration in primary
neurons and in mouse brain. Our data therefore suggest that
small proteins binding the N-terminus of α-synuclein
monomers are promising strategies to modify disease
progression in Parkinson's disease.},
keywords = {molecular chaperones (Other) / nanobodies (Other) /
pre-formed fibrils (Other) / protein aggregation (Other) /
α-synuclein (Other)},
cin = {IBI-7},
ddc = {610},
cid = {I:(DE-Juel1)IBI-7-20200312},
pnm = {5244 - Information Processing in Neuronal Networks
(POF4-524) / BETACONTROL - Control of amyloid formation via
beta-hairpin molecular recognition features (726368)},
pid = {G:(DE-HGF)POF4-5244 / G:(EU-Grant)726368},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:34326719},
pmc = {pmc:PMC8313869},
UT = {WOS:000878869900001},
doi = {10.3389/fnins.2021.696440},
url = {https://juser.fz-juelich.de/record/909067},
}