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@ARTICLE{Comini:910204,
author = {Comini, Maddalena and Sierra-Marquez, Juan and Guzman,
Gustavo and Franzen, Arne and Willuweit, Antje and Katona,
Istvan and Hidalgo, Patricia and Fahlke, Christoph and
Guzman, Raul E.},
title = {{CLC} {A}nion/{P}roton {E}xchangers {R}egulate {S}ecretory
{V}esicle {F}illing and {G}ranule {E}xocytosis in
{C}hromaffin {C}ells},
journal = {The journal of neuroscience},
volume = {42},
number = {15},
issn = {0270-6474},
address = {Washington, DC},
publisher = {Soc.},
reportid = {FZJ-2022-03681},
pages = {3080-3095},
year = {2022},
abstract = {ClC-3, ClC-4, and ClC-5 are electrogenic chloride/proton
exchangers that can be found in endosomal compartments of
mammalian cells. Although the association with genetic
diseases and the severe phenotype of knock-out animals
illustrate their physiological importance, the cellular
functions of these proteins have remained insufficiently
understood. We here study the role of two Clcn3 splice
variants, ClC-3b and ClC-3c, in granular exocytosis and
catecholamine accumulation of adrenal chromaffin cells using
a combination of high-resolution capacitance measurements,
amperometry, protein expression/gene knock out/down, rescue
experiments, and confocal microscopy. We demonstrate that
ClC-3c resides in immature as well as in mature secretory
granules, where it regulates catecholamine accumulation and
contributes to the establishment of the readily releasable
pool of secretory vesicles. The lysosomal splice variant
ClC-3b contributes to vesicle priming only with low
efficiency and leaves the vesicular catecholamine content
unaltered. The related Cl−/H+ antiporter ClC-5 undergoes
age-dependent downregulation in wild-type conditions. Its
upregulation in Clcn3−/− cells partially rescues the
exocytotic mutant defect. Our study demonstrates how
different CLC transporters with similar transport functions,
but distinct localizations can contribute to vesicle
functions in the regulated secretory pathway of granule
secretion in chromaffin cells.},
cin = {INM-4 / IBI-1 / IBI-7},
ddc = {610},
cid = {I:(DE-Juel1)INM-4-20090406 / I:(DE-Juel1)IBI-1-20200312 /
I:(DE-Juel1)IBI-7-20200312},
pnm = {5253 - Neuroimaging (POF4-525) / 5241 - Molecular
Information Processing in Cellular Systems (POF4-524)},
pid = {G:(DE-HGF)POF4-5253 / G:(DE-HGF)POF4-5241},
typ = {PUB:(DE-HGF)16},
pubmed = {35241492},
UT = {WOS:000789016600003},
doi = {10.1523/JNEUROSCI.2439-21.2022},
url = {https://juser.fz-juelich.de/record/910204},
}