% IMPORTANT: The following is UTF-8 encoded. This means that in the presence
% of non-ASCII characters, it will not work with BibTeX 0.99 or older.
% Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or
% “biber”.
@ARTICLE{Neudecker:21070,
author = {Neudecker, P. and Robustelli, P. and Cavallli, A. and
Walsh, P. and Lundstrom, P. and Zarrine-Afsar, A. and
Sharpe, S. and Vendruscolo, M. and Kay, LE.},
title = {{S}tructure of an intermediate state in protein folding and
aggregation},
journal = {Science},
volume = {336},
issn = {0036-8075},
address = {Washington, DC [u.a.]},
publisher = {American Association for the Advancement of Scienc},
reportid = {PreJuSER-21070},
pages = {362 - 366},
year = {2012},
note = {We thank J. Forman-Kay and A. Davidson for providing
laboratory space. S.S. and L.E.K. hold Canada Research
Chairs in Biochemistry. P.R. was funded by a Gates Cambridge
Scholarship and an NSF Graduate Research Fellowship, and
P.W. is funded by a Natural Sciences and Engineering
Research Council of Canada (NSERC) Canada Graduate
Scholarship. This work was supported by grants from the
NSERC and the Canadian Institutes of Health Research
(L.E.K). The ensembles of 10 structures each representing
the A39V/N53P/V55L Fyn SH3 domain native state from
Ser<SUP>1</SUP> to Asp<SUP>59</SUP> and the folding
intermediate from Ser<SUP>1</SUP> to Ala<SUP>56</SUP> have
been deposited with the Protein Data Bank (accession codes
2LP5 and 2L2P, respectively).},
abstract = {Protein-folding intermediates have been implicated in
amyloid fibril formation involved in neurodegenerative
disorders. However, the structural mechanisms by which
intermediates initiate fibrillar aggregation have remained
largely elusive. To gain insight, we used relaxation
dispersion nuclear magnetic resonance spectroscopy to
determine the structure of a low-populated, on-pathway
folding intermediate of the A39V/N53P/V55L (A, Ala; V, Val;
N, Asn; P, Pro; L, Leu) Fyn SH3 domain. The carboxyl
terminus remains disordered in this intermediate, thereby
exposing the aggregation-prone amino-terminal β strand.
Accordingly, mutants lacking the carboxyl terminus and thus
mimicking the intermediate fail to safeguard the folding
route and spontaneously form fibrillar aggregates. The
structure provides a detailed characterization of the
non-native interactions stabilizing an aggregation-prone
intermediate under native conditions and insight into how
such an intermediate can derail folding and initiate
fibrillation.},
keywords = {Amyloid: chemistry / Animals / Chickens / Hydrogen Bonding
/ Models, Molecular / Molecular Dynamics Simulation / Mutant
Proteins: chemistry / Nuclear Magnetic Resonance,
Biomolecular / Protein Conformation / Protein Folding /
Protein Structure, Secondary / Proto-Oncogene Proteins
c-fyn: chemistry / Proto-Oncogene Proteins c-fyn: genetics /
Thermodynamics / src Homology Domains / Amyloid (NLM
Chemicals) / Mutant Proteins (NLM Chemicals) /
Proto-Oncogene Proteins c-fyn (NLM Chemicals) / J (WoSType)},
cin = {ICS-6},
ddc = {500},
cid = {I:(DE-Juel1)ICS-6-20110106},
pnm = {Funktion und Dysfunktion des Nervensystems / BioSoft:
Makromolekulare Systeme und biologische
Informationsverarbeitung},
pid = {G:(DE-Juel1)FUEK409 / G:(DE-Juel1)FUEK505},
shelfmark = {Multidisciplinary Sciences},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:22517863},
UT = {WOS:000302995400051},
doi = {10.1126/science.1214203},
url = {https://juser.fz-juelich.de/record/21070},
}