TY - JOUR
AU - Kuzkina, Anastasia
AU - Panzer, Celine
AU - Seger, Aline
AU - Schmitt, Daniela
AU - Rößle, Jonas
AU - Schreglmann, Sebastian R.
AU - Knacke, Henrike
AU - Salabasidou, Elena
AU - Kohl, Antonia
AU - Sittig, Elisabeth
AU - Barbe, Michael
AU - Berg, Daniela
AU - Volkmann, Jens
AU - Sommer, Claudia
AU - Oertel, Wolfgang H.
AU - Schaeffer, Eva
AU - Sommerauer, Michael
AU - Janzen, Annette
AU - Doppler, Kathrin
TI - Dermal Real‐Time Quaking‐Induced Conversion Is a Sensitive Marker to Confirm Isolated Rapid Eye Movement Sleep Behavior Disorder as an Early α‐Synucleinopathy
JO - Movement disorders
VL - 38
IS - 6
SN - 0885-3185
CY - New York, NY
PB - Wiley
M1 - FZJ-2023-01616
SP - mds.29340
PY - 2023
AB - ABSTRACT:Background:Skin biopsy is apotential tool for the premortem confirmation of anα-synucleinopathy.Objective:The aim was to assess the aggregationassay real-time quaking-induced conversion (RT-QuIC)of skin biopsy lysates to confirm isolated rapid eyemovement sleep behavior disorder (iRBD) as anα-synucleinopathy.Methods:Skin biopsies of patients with iRBD,Parkinson’s disease (PD), and controls were analyzedusing RT-QuIC and immunohistochemical detection ofphospho-α-synuclein.Results:α-Synuclein aggregation was detected in97.4% of iRBD patients (78.4% of iRBD biopsies),87.2% of PD patients (70% of PD biopsies), and 13%of controls (7.9% of control biopsies), with a higherseeding activity in iRBD compared to PD. RT-QuICwas more sensitive but less specific thanimmunohistochemistry.Conclusions:Dermal RT-QuIC is a sensitive methodto detectα-synuclein aggregation in iRBD, and highseeding activity may indicate a strong involvement ofdermal nervefibers in these patients. © 2023 TheAuthors.Movement Disorderspublished by WileyPeriodicals LLC on behalf of International Parkinsonand Movement Disorder Society.Key Words:rapid eye movement sleep behavior dis-order;α-synuclein; Parkinson’s disease; real-timequaking-induced conversion; skin biopsy
LB - PUB:(DE-HGF)16
C6 - 36750755
UR - <Go to ISI:>//WOS:000930736600001
DO - DOI:10.1002/mds.29340
UR - https://juser.fz-juelich.de/record/1005762
ER -